Peran Dukungan Keluarga terhadap Kualitas Hidup Penderita Hemofilia
Keywords:
dukungan keluarga, hemofiliaAbstract
Hemofilia A dan B merupakan gangguan perdarahan yang diturunkan. Gangguan ini akibat kurangnya protein koagulasi faktor VIII pada hemofilia jenis A dan IX pada hemofilia jenis B. Perdarahan sendi dijumpai 70-80% di area pergelangan kaki, siku, dan lutut. Perdarahan sendi yang berulang menyebabkan cedera jaringan sinovial, tulang, dan tulang rawan. Hal ini memberikan efek gangguan pada aktivitas sehari-harinya. Dukungan keluarga mampu memengaruhi kesehatan fisik dan mental melalui pembentukan emosional, peningkatan kognitif, dan pembentukan perilaku. Tujuan penelitian ini untuk mengetahui peran dukungan keluarga terhadap kualitas hidup penderita hemofilia. Desain penelitian menggunakan deskriptif analitik dengan pendekatan cross sectional. Lokasi penelitian di Himpunan Masyarakat Hemofilia Indonesia Yogyakarta. Perhitungan sampel analitik korelatif ditemukan sebanyak 42 responden. Analisis data menggunakan uji nonparametrik Somers’d dengan derajat kemaknaan α = 0,05. Dukungan keluarga penderita hemofilia sebagian besar adalah tinggi sebanyak 35 (83,3%) responden. Kualitas hidup penderita hemofilia sebagian besar baik sebanyak 29 (69%) responden. Ada hubungan dukungan keluarga dengan kualitas hidup penderita hemofilia (p-value:0,005) dengan hubungan keeratan sedang (0,66). Hubungan dukungan keluarga dengan variabel domain kualitas hidup menunjukkan ada hubungan yang signifikan dengan keeratan cukup untuk domain keterbatasan fisik dan keeratan kuat untuk domain fungsi fisik.
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